نتایج جستجو برای: mowat syndrome

تعداد نتایج: 621961  

2016
Qian Jiang Tao Zhang Shuo Wang Ping Xiao Zhen Zhang Yinan Ma Wei Cheng Lin Su Hong Pan Qi Li Long Li

Mowat-Wilson syndrome (MWS, MIM #235730) is a rare genetic disorder characterized by moderate-tosevere mental retardation, a recognizable facial gestalt and multiple congenital anomalies. The striking facial phenotype in addition to other features such as microcephaly, congenital heart defects, Hirschsprung disease (HSCR), severely delayed motor/speech development, seizures, short stature, corp...

2012
Aurélien Capitan Aurélie Allais-Bonnet Alain Pinton Brigitte Marquant-Le Guienne Daniel Le Bourhis Cécile Grohs Stéphan Bouet Laëtitia Clément Laura Salas-Cortes Eric Venot Stéphane Chaffaux Bernard Weiss Arnaud Delpeuch Guy Noé Marie-Noëlle Rossignol Sarah Barbey Dominique Dozias Emilie Cobo Harmonie Barasc Aurélie Auguste Maëlle Pannetier Marie-Christine Deloche Emeline Lhuilier Olivier Bouchez Diane Esquerré Gérald Salin Christophe Klopp Cécile Donnadieu Céline Chantry-Darmon Hélène Hayes Yves Gallard Claire Ponsart Didier Boichard Eric Pailhoux

Polled and Multisystemic Syndrome (PMS) is a novel developmental disorder occurring in the progeny of a single bull. Its clinical spectrum includes polledness (complete agenesis of horns), facial dysmorphism, growth delay, chronic diarrhea, premature ovarian failure, and variable neurological and cardiac anomalies. PMS is also characterized by a deviation of the sex-ratio, suggesting male letha...

Journal: :Journal of medical genetics 2009
S Jaillard C Dubourg M Gérard-Blanluet A Delahaye L Pasquier C Dupont C Henry A-C Tabet J Lucas A Aboura V David B Benzacken S Odent E Pipiras

BACKGROUND Genome-wide screening of patients with mental retardation using array comparative genomic hybridisation (CGH) has identified several novel imbalances. With this genotype-first approach, the 2q22.3q23.3 deletion was recently described as a novel microdeletion syndrome. The authors report two unrelated patients with a de novo interstitial deletion mapping in this genomic region and pre...

Journal: :The Journal of the Anthropological Institute of Great Britain and Ireland 1890

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