Priapism is a prolonged involuntary erection that can have severe complications if left untreated. Ischaemic priapism very rare in children and requires urgent intervention to prevent permanent erectile dysfunction penile shortening. It be caused by ischaemia sickle cell anaemia, leukaemia, trauma, drugs, or idiopathy. Homocystinuria autosomal recessive disorder cause hyperhomocysteinemia hyper...