نتایج جستجو برای: hemophagocytic syndrome

تعداد نتایج: 624474  

Journal: :Journal of clinical and experimental hematopathology : JCEH 2014
Rie Tabata Ryoji Yasumizu Chiharu Tabata Masaru Kojima

It is well known that some B-cell lymphomas are accompanied by a prominent epithelioid cell response, caused by activated macrophages, such as marginal zone B-cell lymphoma of a mucosa-associated lymphoid tissue. We investigated six bone marrow samples from four cases of Waldenström's macroglobulinemia and report a unique observation that large conjugates of tumor cells around a macrophage were...

2014
Vitor Ribeiro Paes Patrícia Picciarelli de Lima Sheila Aparecida Coelho Siqueira

Hepatosplenic T-cell lymphoma (HSTCL) is a rare non-Hodgkin lymphoma, marked by liver, spleen, and bone marrow sinusoidal infiltration, with an aggressive clinical course, which represents a difficult diagnostic task for clinicians and pathologists. Another equally severe and challenging condition is the hemophagocytic lymphohistiocytosis (also called hemophagocytic syndrome [HS]), which is oft...

Journal: :Haematologica 1995
A M Marmont M Spriano

he fulminant hemophagocytic syndromes, as recently defined by Cline, are aggressive and often fatal disorders, most frequent in children but occurring in all ages, that are characterized by fever, systemic symptoms, jaundice, multiple organ failure, coagulopathy, and phagocytosis of blood elements with cytopenias. Death may occur in up to 40% of cases. A distinction is generally made between fa...

Journal: :Turk pediatri arsivi 2016
Seçil Arslansoyu Çamlar Mustafa Kır Ceyda Aydoğan Şebnem Yılmaz Bengoa Mehmet Atilla Türkmen Alper Soylu Salih Kavukçu

Salmonella infections are observed frequently in the childhood age group and mostly characterized with gastrointestinal findings. Extraintestinal involvement is observed rarely (8%) (1). Renal involvement has been defined in approximately 3% of the patients. Pyelonephritis, cystitis, hemolytic uremic syndrome, acute renal failure and rarely glomerulonephritis have been reported as urinary syste...

Journal: :Haematologica 2010
Jan Rohr Karin Beutel Andrea Maul-Pavicic Thomas Vraetz Jens Thiel Klaus Warnatz Ilka Bondzio Ute Gross-Wieltsch Michael Schündeln Barbara Schütz Wilhelm Woessmann Andreas H Groll Brigitte Strahm Julia Pagel Carsten Speckmann Gritta Janka Gillian Griffiths Klaus Schwarz Udo zur Stadt Stephan Ehl

BACKGROUND Familial hemophagocytic lymphohistiocytosis is a genetic disorder of lymphocyte cytotoxicity that usually presents in the first two years of life and has a poor prognosis unless treated by hematopoietic stem cell transplantation. Atypical courses with later onset and prolonged survival have been described, but no detailed analysis of immunological parameters associated with typical v...

2002
Je-Jung Lee Ik-Joo Chung Dong-Hyeon Shin Sang-Hee Cho Duck Cho Dong-Wook Ryang Ali S. Khan Hyeoung-Joon Kim

Hemophagocytic lymphohistiocytosis--which is associated with a variety of infections, malignant neoplasms, autoimmune diseases, and immunodeficiencies--is an uncommon syndrome with a rapidly fatal outcome. We describe the first case of hemorrhagic fever with renal syndrome due to Hantaan virus presenting with reactive hemophagocytosis.

2012
Lidija DOKMANOVIĆ Nada KRSTOVSKI Predrag RODIĆ Dragana JANIĆ

www.paediatricstoday.com Visceral leishmaniasis (VL) is caused by the dissemination of the protozoan parasite Leishmania donovani throughout the reticuloendothelial system. This systemic disease may mimic or lead to several types of hematological disorders including hemophagocytic lymphohistiocytosis (HLH). Infection associated hemophagocytic syndrome caused by Leishmania is very rare and diffi...

2016
Maria Koshy Ajay Kumar Mishra Bhumi Agrawal Akhil Rajendra Kurup Samuel George Hansdak

Dengue is a common acute viral febrile illness in the tropics. Although the usual presentation is that of a self-limiting illness, its complications are protean. We report a 29-year-old man who presented with an acute febrile illness and was diagnosed with dengue hemorrhagic fever. Despite appropriate supportive therapy, the patient initially improved, but subsequently had clinical deterioratio...

Journal: :Indian pediatrics 1994
B R Agarwal Z Currimbhoy

Histiocytic syndromes in children are divided into 3 classes: (i) Langerhans-cell histiocytosis (LCH) or Histiocytosis-X (HX), (ii) Hemophagocytic syndromes—Familial erythrophagocytic lymphohistiocytosis (FEL) and infection-associated hemophagocytic syndrome (IAHS) due to viruses (VAHS), and occasionally bacterial, fungal or parasitic, and (iii) Malignant histiocytic disorders(l). The lesional ...

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