BACKGROUND Nephropathic cystinosis is a rare inherited metabolic disorder leading to progressive renal failure and extra-renal comorbidity. The prognosis relies on early adherence to cysteamine treatment and symptomatic therapies. Developing nations [DiN] experience many challenges for management of cystinosis. The aim of this study was to assess the management characteristics in DiN compared w...

Gunther Auer, Vito Giannini, István Gódor, Magnus Olsson, Muhammad Ali Imran, Dario Sabella, Manuel J. Gonzalez Oliver Blume, Albrecht Fehske, Jose Alonso Rubio, Pål Frenger, Claude Desset DOCOMO Euro-Labs, D-80687 Munich, Germany IMEC, Leuven, Belgium Ericsson Research, Budapest H-1117, Hungary Ericsson Research, SE-164 80 Stockholm, Sweden CCSR University of Surrey, Guildford GU2 7XH, UK Tele...

62 Improvement in Power Efficiency of Injection Molding Machine by Reduction in Plasticization Losses Muhammad Khan, Mechanical Engineering Department, HITEC University, Taxila, Pakistan Nizar Ullah Khan, Department of Mechanical Engineering, Oakland University, Rochester, MI, USA Muhammad Junaid Aziz, Mechanical Engineering Department, University of Engineering & Technology, Taxila, Pakistan H...

Muhammad Burhan Ud din Janjua, Inayat Ullah Khan Department of Neurosurgery, Shifa International Hospital, Islamabad, Pakistan. ABSTRACT Objective To present the local experience of fat graft use for sella closure in case of intraoperative CSF leak to prevent the post operative CSF rhinorrhea. Patient and Methods We retrospectively studied 22 cases operated for pituitary adenomas from 2004 to 2...

PURPOSE The aim of this work was to implement, validate, and compare two procedures for routine image quality (IQ) assurance in dental cone-beam computed tomography (CBCT): 1. the German standard DIN 6868 - 161 introduced in 2013 and 2. the established standard IEC 61,223 - 3-5 for clinical CT x-ray equipment referenced as "DIN" and "IEC" below. MATERIALS AND METHODS The approximated in-plane...

Sitele moleculare din carbon (CMS) sunt adsorbanţi carbonici de mare importanţă. Această lucrare prezintă rezultatele studiului privind prepararea sitelor moleculare din carbon şi modificarea structurii porilor. Proprietăţile sitelor moleculare ale varietăţilor de cărbuni au fost studiate prin măsurarea capacităţii de adsorbţie dinamică a dioxidului de carbon utilizând sistemul PSA ( adsorbţia ...

Falling and being in love is a cross-cultural universal. The poet Khwaja Šams ud-Din Muhammad Hafez-e Širazi, or simply Hafez (14 th century D.C.), an important influence for both Persian and European culture, is noted for his love poetry. The first aim of the present study was to check to what extent items of a current questionnaire of love match themes of love found in Hafez‘ poetry. Then, we...

We present new estimates of emissions of nitrous oxide (N2O) from rivers and estuaries, using the NEWS-DIN model. NEWS-DIN is a model of the global transport of dissolved inorganic nitrogen (DIN) by rivers to coastal waters (Dumont et al. forthcoming). It calculates DIN export rates as a function of watershed characteristics, including human influences. We used the calculated DIN export rates b...

Environmental cues transduced by an endocrine network converge on Caenorhabditis elegans nuclear receptor DAF-12 to mediate arrest at dauer diapause or continuous larval development. In adults, DAF-12 selects long-lived or short-lived modes. How these organismal choices are molecularly specified is unknown. Here we show that coregulator DIN-1 and DAF-12 physically and genetically interact to in...