Background: Chronic diseases in children lead to failure in the development of self-esteem and productivity. Self-efficacy decreases as one’s behaviors become more complex and difficult to deal with. Storytelling is an observational learning method, which is effective in improving self-efficacy. Aim: to determine the effects of storytelling on self-efficacy in children with thalassemia (aged 7-...

Sickle cell anemia (SCA) is a disease characterized by abnormal red blood rheology. Because of their effects on HbS polymerization and deformability, alpha-thalassemia the residual HbF level are known genetic modifiers disease. The aim our study was to determine if number quantitative trait loci (QTL) would also favor specific sub-phenotype SCA as it case for alpha-thalassemia. Our results conf...

Thalassemia and Sickle Cell Disease (SCD) both are genetic blood disorders occurring by destruction in red blood cells (RBCs). Every year about 300,000 infants worldwide are born with Thalassemia syndrome (30 per cents) and sickle cell anaemia (70 per cents. Globally, the percentage of carriers of Thalassemia is greater than that of carriers of SCA, but because of the high frequency of the sick...

Abstract Background Thalassaemia, a hereditary haemoglobin disorder, is major public health concern in some parts of the world. Although Bangladesh world’s thalassaemia belt, information on this disease scarce. Additionally, awareness life threatening, but potentially preventable surprisingly poor. However, mass pivotal for development an effective preventive strategy. In context, understanding...

OBJECTIVES To analyze the frequency of β(S)-globin haplotypes and alpha-thalassemia, and their influence on clinical manifestations and the hematological profile of children with sickle cell anemia. METHOD The frequency of β(S)-globin haplotypes and alpha-thalassemia and any association with clinical and laboratorial manifestations were determined in 117 sickle cell anemia children aged 3-71 ...

BACKGROUND/HYPOTHESIS Creeping monotony in the treatment provides minimal motivation for children with beta-thalassemia major, leading to noncompliance for adequate blood transfusions and iron chelation therapy. This study was envisaged to formulate a clinical compliance score and correlate the score with their linear growth velocity and weight gain. MATERIALS AND METHODS A prospective longit...

Thalassemias are inherited blood disorders. In 2011, there was no clear situation regarding the number of thalassemia or other hemoglobinopathy patients in Romania. The luck of information has led to an increased number of patients registered by Fundeni Hospital, Bucharest in the last years. The main goal of this article is to underline the importance of implementing a screening program in Roma...

The study aimed to determine the effect of an educational program on parents' knowledge about chelation therapy, and nutrition their children with beta thalassemia major. A quasi experimental was carried out at Thalassemia Center in Al-Najaf City during periods 25 ͭ ͪ February 2021 15 March 2022. Non-probability (purposive) sample (70) parents were selected from center (38 mothers 32 fathers).The...