CANTRELL SYNDROME IS A VERY RARE CONGENITAL DISEASE ASSOCIATING FIVE FEATURES: a midline, upper abdominal wall disorder, lower sternal abnormality, anterior diaphragmatic defect, diaphragmatic pericardial abnormality, and congenital abnormalities of the heart. In this paper, we report a case of partial Cantrell's syndrome with left ventricular diverticulum, triatrial situs solitus, ventricular ...

The pentalogy of Cantrell was first described by Cantrell et al in 1958, who reported 5 cases with this anomaly [1]. The findings included a lower sternum defect, a midline supraumblical thoracoabdominal wall defect, a defect of the anterior diaphragm, a defect of the diaphragmatic pericardium and congenital cardiac anomalies [1,2]. The pentalogy is associated with very poor prognosis and there...

discussion children with congenital heart disease are at risk of acquiring gram-negative endocarditis even if they have not had other predisposing factors. case presentation in this study a ten-year-old boy with ventricular septal defect, who was not immune compromised and acquired klebsiella endocarditis is introduced. the patient had a favorable response to medical treatment and underwent a s...

Chylopericardium after intrapericardial cardiac operations is extremely rare. We present an unusual case of postoperative chylopericardium with cardiac tamponade following atrial septal defect repair, and we comment on the clinical course and treatment.

Iatrogenic aortic valve injury during non-aortic cardiac surgery is an infrequent complication. regurgitation (AR) has been reported after mitral repair, septal myomectomy, closure of the ventricular defect, and atrial defect repair. Various causes have for AR surgery. Perforation leaflet a common cause AR. Other are tension retraction due to inadvertent suture placement. A few previous case re...

OBJECTIVE To define by three dimensional echocardiography the pattern and potential determinants of contraction of a secundum atrial septal defect through the cardiac cycle, and to evaluate the possibility of using cross sectional transthoracic and transoesophageal imaging to assess the dynamic nature of the defect. DESIGN Three dimensional echocardiography was performed using a multiplane tr...

Eighty seven of 100 consecutive recruits referred for cardiac assessment of fitness to serve had heart murmurs. Seven of these were rejected as having significant cardiac disease. One with a diagnosis of hypertrophic cardiomyopathy would have been placed at considerable risk had he been exposed to the physical stress of military training. The remaining 6 rejected had conditions which could have...

Heterozygous mutations in NKX2.5, a homeobox transcription factor, were reported to cause secundum atrial septal defects and result in atrioventricular (AV) conduction block during postnatal life. To further characterize the role of NKX2.5 in cardiac morphogenesis, we sought additional mutations in groups of probands with cardiac anomalies and first-degree AV block, idiopathic AV block, or tetr...

background: cardiac involvement in systemic sclerosis (ssc) is more prevalent than previously thought. in this study, the frequency and severity of cardiovascular involvement were assessed in ssc patients referred to firouzgar hospital. methods: fifty-eight patients with ssc, selected from the data bank of ssc patients, were reviewed for the frequency and severity of 8 organ involvements in thi...

THE hemodynamic state, blood gas levels, blood volumes, and residual shunts soon after repair of atrial septal defect, ventrieular septal defect, and tetralogy of Fallot have been described in previous publications.1-4 Similar data have now been obtained after open operation for acquired disease of the aortic valve, and additional measurements of atrial pressures after repair of ventricular sep...