نتایج جستجو برای: aspartoacylase deficiency

تعداد نتایج: 137211  

Journal: :Molecular therapy : the journal of the American Society of Gene Therapy 2013
Seemin Seher Ahmed Huapeng Li Chunyan Cao Elif M Sikoglu Andrew R Denninger Qin Su Samuel Eaton Ana A Liso Navarro Jun Xie Sylvia Szucs Hongwei Zhang Constance Moore Daniel A Kirschner Thomas N Seyfried Terence R Flotte Reuben Matalon Guangping Gao

Canavan's disease (CD) is a fatal pediatric leukodystrophy caused by mutations in aspartoacylase (AspA) gene. Currently, there is no effective treatment for CD; however, gene therapy is an attractive approach to ameliorate the disease. Here, we studied progressive neuropathology and gene therapy in short-lived (≤ 1 month) AspA(-/-) mice, a bona-fide animal model for the severest form of CD. Sin...

Abstract Background: Iron deficiency is the most common nutritional deficiencies in the world. So that 15% of the total world population is involved.  The present study examined the association between iron deficiency anemia and primary hypothyroidism and the prevalence of iron deficiency anemia and primary hypothyroidism, respectively, in patients with iron deficiency anemia and primar...

Journal: :iranian journal of allergy, asthma and immunology 0
mohammad saeid rahiminejad department of pediatrics, pediatrics center of excellence, children's medical center, tehran university of medical sciences, tehran, iran mehrdad mirmohammad sadeghi department of pediatrics, pediatrics center of excellence, children's medical center, tehran university of medical sciences, tehran, iran payam mohammadinejad research center for immunodeficiencies, tehran university of medical sciences, tehran, iran bamdad sadeghi research center for immunodeficiencies, tehran university of medical sciences, tehran, iran hassan abolhassani research center for immunodeficiencies, tehran university of medical sciences, tehran, iran mohammad mehdi dehghani firoozabadi research center for immunodeficiencies, tehran university of medical sciences, tehran, iran

coincidence of autoimmune diseases such as immune thrombocytopenic purpura (itp) with  immunodeficiencies has  been  reported  previously in  patients  who  suffered  from primary antibody deficiency (pad). but there is no original study on immunological profiles of itp patients to find out their probable immune deficiency. in this case-control study, itp patients’ humoral immunity was investig...

In this paper, some results of Singh, Gopalakrishna and Kulkarni (1970s) have been extended to higher order derivatives. It has been shown that, if $sumlimits_{a}Theta(a, f)=2$ holds for a meromorphic function $f(z)$ of finite order, then for any positive integer $k,$ $T(r, f)sim T(r, f^{(k)}), rrightarrowinfty$ if $Theta(infty, f)=1$ and $T(r, f)sim (k+1)T(r, f^{(k)}), rrightarrowinfty$ if $Th...

Journal: :iranian journal of pediatric hematology and oncology 0
mehran karimi hematology research center, shiraz university of medical sciences, shiraz, iran nader cohan hematology research center, shiraz university of medical sciences, shiraz, iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شیراز (shiraz university of medical sciences) vincenzo de sanctis pediatric and adolescent outpatient clinic, quisisana hospital, ferrara, italyسازمان اصلی تایید شده: دانشگاه علوم پزشکی شیراز (shiraz university of medical sciences)

this study presented a mini review on folic acid deficiency and recommendations for its supplementation in thalassemia intermedia (ti). ti is a clinical condition which lies between thalassemia major and thalassemia minor. although ti patients may not need regular blood transfusion, precise diagnosis and management are critical for the prevention of clinical complications and quality of life im...

Journal: :iranian journal of child neurology 0
razieh fallah 1. department of pediatric neurlogy, growth disorders of children research center, shahid sadoughi university of medical sciences, yazd, iran behnaz tirandazi 2. shahid sadoughi university of medical sciences, yazd, iran farzad ferdosian 3. subspecialty in pediatric infectious disease, department of pediatrics, shahid sadoughi university of medical sciences, yazd, iran nafisah fadavi 2. shahid sadoughi university of medical sciences, yazd, iran

how to cite this article: fallah r, tirandazi f, ferdosian f, fadavi n. iron deficiency and iron deficiency anemia in children with first attack of seizure and on healthy control group : a comparative study. iran j child neurol. 2014 summer;8(3): 18-23.   abstract objective seizures are the most common pediatric neurologic problem. research of the association between iron deficiency and seizure...

Journal: :acta medica iranica 0
mehrdad shakiba department of pediatric nephrology, shahid sadoughi hospital, school of medicine, shahid sadoughi university of medical sciences, yazd, iran. zahra nafei department of pediatric, shahid sadoughi hospital, school of medicine, shahid sadoughi university of medical sciences, yazd, iran. mohammad hassan lotfi department of clinical epidemiology, shahid sadoughi hospital, school of medicine, shahid sadoughi university of medical sciences, yazd, iran. ahmad shajari department of pediatric nephrology, shahid sadoughi hospital, school of medicine, shahid sadoughi university of medical sciences, yazd, iran.

vitamin d is essential for growth and vitamin d deficiency is important issue in adolescent girls as they have a limited rapid growth period .this cross sectional study was done on 167 female students in secondary guidance school in 2006. growth parameters, taking supplementary vitamin d, using sunscreen creams and the type of housing and their avoidance from exposure to sunlight was recorded. ...

Journal: :iranian journal of blood and cancer 0
adel baghersalimi bahram darbandi hamid alizadeh

platelet adherence surrounding leucocytes in a rosette formation or platelet satellitism is a rare phenomenon. this finding has been observed almost exclusively in ethylenediaminetetraacetic acid treated blood at room temperature. the mechanism underlying this phenomenon is not fully understood. in many reports of platelet satellitism platelets clump to polymorphonuclear neutrophils in healthy ...

Journal: :iranian journal of allergy, asthma and immunology 0
mohammad hasan moradinejad department of rheumatology, children’s medical center, tehran university of medical sciences, tehran,iran ali hoseinpoor rafati immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran maryam ardalan immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran mahnaz rabiei immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran maryam farghadan immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran mohammad taghi haghi ashtiani clinical and anatomical pathology, children medical center, tehran university of medical sciences, tehran, iran

the purpose of this study was to investigate any association between iga deficiency (igad) and juvenile rheumatoid arthritis (jra) among iranian children. this case-control study was carried out on 83 children who were diagnosed as jra according to american college of rheumatology (acr) criteria; patients were admitted at the rheumatology clinic of children's medical center, (tehran). serum imm...

Journal: :iranian red crescent medical journal 0
sadaf alipour research development center, arash women’s hospital, tehran university of medical sciences, tehran, ir iran azin saberi department of surgery, arash women’s hospital, tehran university of medical sciences, tehran, ir iran akram seifollahi pathology department, arash women’s hospital, tehran university of medical sciences, tehran, ir iran nooshin shirzad endocrinology and metabolism research institute, dr. shariati hospital, tehran university of medical sciences, tehran, ir iran ladan hosseini research development center, arash women’s hospital, tehran university of medical sciences, tehran, ir iran; research development center, arash women’s hospital, tehran university of medical sciences, tehran, ir iran. tel: +98-2177719922; fax: +98-2177883196

background several studies indicated that there is a high prevalence of vitamin d deficiency in middle east countries. objectives the aim of this study was to determine the prevalence and assess some risk factors of vitamin d deficiency among women attending our clinics in tehran, the capital of iran. patients and methods five hundred and thirty-eight women aged 20-80 years were entered in this...

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