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Background: Aplasia cutis congenita (ACC) is a rare condition regarded as congenital absence of the epidermis, dermis, and in some cases, subcutaneous tissues newborn. The pathogenic mechanism unclear, although has been described result disrupted development or degeneration skin utero. ACC may be observed with fetus papyraceous (FP). Case Presentation: We report case an 8-hour-old newborn femal...

Adams-Oliver syndrome (AOS) is a rare congenital disorder, characterized by aplasia cutis congenita (ACC) of the scalp and variable degrees of terminal transverse limb defects. In this article, a newborn infant diagnosed as AOS for a large scalp defect, acrania, and finger malformations is presented. The patient was hospitalized and the scalp defect was successfully repaired with several surgic...

Aplasia cutis congenita is a rare malformation characterized by localized congenital absence of the skin. It rarely occurs on the trunk and limbs, and can occur in isolation or as part of a heterogeneous group of syndromes. We report a case of a 4-day-old boy with a 5.6-cm- diameter tumor, with a central crust, non-indurate and no inflammatory rim; localized on the scalp and a small, atrophic h...