نتایج جستجو برای: 46 xy female

تعداد نتایج: 351927  

Journal: :Journal of the College of Physicians and Surgeons--Pakistan : JCPSP 2014
Irum Atta Mohsina Ibrahim Arit Parkash Saira Waqar Lone Yasir Naqi Khan Jamal Raza

OBJECTIVE To do clinical, hormonal and chromosomal analysis in undervirilized male / XY disorder of sex development and to make presumptive etiological diagnosis according to the new Disorder of Sex Development (DSD) classification system. STUDY DESIGN Case series. PLACE AND DURATION OF STUDY Endocrine Unit at National Institute of Child Health, Karachi, Pakistan, from January 2007 to Decem...

2017
Ani Amelia Zainuddin Zaleha Abdullah Mahdy

In Islam, the person with somatic sex ambiguity due to a disorder of sex development (DSD), such as 46,XX congenital adrenal hyperplasia or 46,XY androgen insensitivity, is recognized as khunsa. Two types of khunsa are distinguished: wadhih (discernible) and musykil (intractable). A recent fatwa (religious edict) in Malaysia decreed that it is permissible for male-assigned patients from these t...

Journal: :Arquivos brasileiros de endocrinologia e metabologia 2010
Juliana Gabriel Ribeiro de Andrade Gil Guerra-Júnior Andréa Trevas Maciel-Guerra

The objective of this study was to describe the change in diagnosis and prognosis of a child with testicular dysgenesis and 46,XY karyotype after detection of a 45,X cell line and to discuss the difficulties caused by the terms mixed gonadal dysgenesis (MGD) and XY partial gonadal dysgenesis (XYPGD). One case was reported including clinical and laboratory findings of a child of 41-day-old infan...

Journal: :Human molecular genetics 2015
Stefan Bagheri-Fam Makoto Ono Li Li Liang Zhao Janelle Ryan Raymond Lai Yukako Katsura Fernando J Rossello Peter Koopman Gerd Scherer Oliver Bartsch Jacob V P Eswarakumar Vincent R Harley

Patients with 46,XY gonadal dysgenesis (GD) exhibit genital anomalies, which range from hypospadias to complete male-to-female sex reversal. However, a molecular diagnosis is made in only 30% of cases. Heterozygous mutations in the human FGFR2 gene cause various craniosynostosis syndromes including Crouzon and Pfeiffer, but testicular defects were not reported. Here, we describe a patient whose...

2014
Akanksha Mehta Anna Mielnik Peter N Schlegel Darius A Paduch

The aim of this study was to design a molecular assay for the diagnosis of Klinefelter syndrome (KS), based on the detection of supernumerary X-chromosomes (X-chs). DNA was extracted from peripheral blood samples of twenty-six 47,XXY males; two 46,XY/47,XXY males; twenty-two 46,XY males; and 15 females; and deaminated. Methylation-specific quantitative polymerase chain reaction (MS-qPCR) was pe...

Journal: :Journal of medical genetics 1976
R L Neu J A Stockman R E Spitzer R H Tomar

An infant with neutropenia, properdin deficiency, and a 46,XY/46,XY,21q- mosaicism is described. It is not known whether these two findings are related to the missing 21q material. The propositus is normal in appearance, and has none of the phenotypic features associated with the G-group deletion syndromes.

2016
Salil Vaniawala Pankaj Gadhia

Chromosomal abnormalities are one of the major causes of infertility in man and woman. A couple with history of recurrent spontaneous abortion (RSA) was referred to our laboratory for chromosomal analysis. The analysis revealed normal 46,XY karyot ype in male and a novel balanced translocation 46,XXt(4;20)(q11;p13) in female partner. This translocation with breakpoints has not been reported in ...

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