نتایج جستجو برای: آمیلوییدوز amyloidoses

تعداد نتایج: 269  

2012
C. Cristina Quarta Rodney H. Falk

The systemic amyloidoses are a group of uncommon diseases characterized by extracellular accumulation of fibrillar proteins, leading to loss of normal tissue architecture and function (1). Light-chain (AL) amyloidosis, which is probably the most frequent form, can potentially involve any organ, but when the heart is affected, the outcome is particularly poor, with a median survival of 4 to 6 mo...

2013
Tobias A. Mattei

the cause of propagation of misfolded proteins in spongiform encephalopathies. In fact, several recent studies (Jucker and Walker, 2011; Hall and Patuto, 2012; Kanouchi et al., 2012) have suggested that the basic proteins implied in a variety of neurodegenerative diseases [like betaamyloid and tau proteins in Alzheimer’s disease (AD), α-synuclein in Parkinson Disease and dementia with Lewy bodi...

Journal: :Journal of medical genetics 1975
P K Thomas

In the absence of biochemical distinctions, the nosography of the inherited amyloidoses must at present depend largely upon clinical subdivisions. In the broad classification adopted here, the disorders have for convenience been grouped according to the anatomical system that is predominantly affected. It is evident that the amyloid syndromes display considerable heterogeneity. However, they ov...

2012
Murat İnanç Cengiz Kuddusi Cengiz

Although recent decades have provided significant advances in our understanding of the pathology and pathogenesis of AA amyloidosis, the mechanism and etiopathological factors promoting amyloidosis are largely unknown (Elimowa et al., 2009). Its pathogenesis is multifactorial, involving many variables such as primary structure of the precursor protein, acute-phase response, the presence of non-...

Journal: :Acta biochimica Polonica 2015
Carlos Polanco José Lino Samaniego Vladimir N Uversky Jorge Alberto Castañón-González Thomas Buhse Marili Leopold-Sordo Alejandro Madero-Arteaga Alicia Morales-Reyes Lourdes Tavera-Sierra Jesus A González-Bernal Miguel Arias-Estrada

There is a natural protein form, insoluble and resistant to proteolysis, adopted by many proteins independently of their amino acid sequences via specific misfolding-aggregation process. This dynamic process occurs in parallel with or as an alternative to physiologic folding, generating toxic protein aggregates that are deposited and accumulated in various organs and tissues. These proteinaceou...

پایان نامه :وزارت علوم، تحقیقات و فناوری - دانشگاه تربیت مدرس - دانشکده علوم پایه 1387

چکیده ندارد.

پایان نامه :وزارت علوم، تحقیقات و فناوری - دانشگاه تحصیلات تکمیلی علوم پایه زنجان - دانشکده زیست شناسی 1392

برخی از بیماری¬ها مانند بیماری آلزایمر و آمیلوئیدی شدن لیزوزیم ناشی از تشکیل تجمع¬های پروتئینی هستند. پپتیدازهای تجزیه کننده¬ی آمیلوئید بتا مانند نپریلایزین و آنزیم تجزیه کننده¬ی انسولین می¬توانند تجمع¬های آمیلوئید بتا را تجزیه کنند. در این پروژه به بررسی اثرات پروتئولیتیکی آنزیم¬های تریپسین و آلفا- کیموتریپسین روی تجمع¬های لیزوزیمی پرداخته شد. روش طیف¬سنجی فلورسانس و میکروسکوپ نیروی اتمی برای ...

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