A Case Report: A Newborn with Severe Ebstein's Anomaly in Hajar Hospital of Shahrekord

Background and Aims: Ebstein’s anomaly is an abnormal displacement downward of Tricuspid valve into the right ventricular, which is accompanied by myopathy of the right ventricular. It is found rarely with the prevalence of approximately 1:20000. Since the diagnosis of this disease in the appropriate position and time, the management of patients is important. This infant with Ebstein’s anomaly is reported as a case report. Hajar Hospital, Shahrekord Methods: The patient was a girl infant born due to heart drop through Cesarean on Nov 20, 2019 achieved G1Ab0L1 with GA = 35w+ 6d. The infant was transferred to the NICU ward of Hajar Hospital due to the Hypotone and HR<100 with NCPAP after initial procedures. The fetal echo and ultrasonography of neonate reordered cardiomegaly, pleural effusion and large ASD. Echocardiogram performed at birth showed severe Einsteinchr('39')s anomaly, PDA, ultra-thin pulmonary and pulmonary valve atresia. Conclusion: The Ebstein’s anomaly is a rare disease with a prevalence of 1:20000 births and based on the severity of involving in patients is caused different symptoms. Recognition and diagnosis on time of the disease and treatment of its complications decreases the rate of mortality.