A Rare Case of Sporadic Inclusion Body Myositis (s-IBM).
نویسندگان
چکیده
Sporadic inclusion body myositis (s-IBM) is an acquired inflammatory myopathy. Clinical presentation is variable. The usual presentation is progressive weakness and atrophy of the arms and leg muscles, especially of the quadriceps femoris which is invariably affected. It is classified under inflammatory myopathies, along with polymyositis and dermatomyositis. We present a case of s-IBM who presented with gradually progressive quadriparesis with characteristic quadriceps wasting and weakness in neck flexors. Electromyography revealed myopathic potential and muscle biopsy revealed features of inclusion body myositis.
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ورودعنوان ژورنال:
- Journal of clinical and diagnostic research : JCDR
دوره 10 1 شماره
صفحات -
تاریخ انتشار 2016