Prenatal Diagnosis and Management of Tricuspid Valve Atresia: A Case Report and Review of Literature

Aim To describe the prenatal features, diagnosis, post-natal follow up and the strategy of treatment of patients suffering from Tricuspid Valve Atresia (TvAtr). Methods We describe a case and its outcome on a three-year follow-up. We review the existing literature on the pre-natal diagnosis, post-natal management and late outcome. Results Based on this case, We present the key findings for diagnosis by fetal echocardiography that include: demonstration of no patent tricuspid valve on the 4-chamber view, no flow across the TV on pulsed or color Doppler flow mapping, small Right Ventricle (RV) with associated inter Ventricular Septal Defect (VSD) and the Great Vessels (GA’s) connectivity to the ventricles (normal related or transposed great vessels). The hypoplastic RV, must give the primary clue leading to follow-up series of scans that can determine the immediate post-natal anatomy and further management of the patient. Conclusion TvAtr can be accurately diagnosed prenatally. The key findings, differential diagnoses and management are discussed. Review of the literature of the disease is provided.