Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
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چکیده
منابع مشابه
Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant ...
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Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise specified (PEComa-NOS), and one of the most common primary sites for PEComa-NOS is the uterus. The ris...
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ژورنال
عنوان ژورنال: Korean Journal of Radiology
سال: 2013
ISSN: 1229-6929,2005-8330
DOI: 10.3348/kjr.2013.14.4.692