Porto-Splenic veins thrombosis and Budd-Chiari syndrome in a patient with essential thrombocythemia – is it always the myeloproliferative neoplasm to blame?
نویسندگان
چکیده
Bone marrow fibrosis leading to dry tap aspiration and often associated with blast crisis has previously been reported in both Chronic myeloid leukemia Primary myelofibrosis.
منابع مشابه
INFERIOR VENA CAVA THROMBOSIS IN A PATIENT WITH ESSENTIAL THROMBOCYTHEMIA
Essential thrombocythemia is a chronic myeloproliferative disorder characterized by a sustained proliferation of megakaryocytes, which leads to increased numbers of circulating platelets. Hemorrhagic and/or thrombotic episodes are frequent, and thrombosis of both veins and arteries may develop. Vessels in unusual sites may be involved, e.g., the hepatic veins, mesenteric veins, and the dig...
متن کاملBudd-Chiari syndrome caused by hepatic vein thrombosis in a patient with myeloproliferative disorder.
We report a 24-year-old Japanese female hospitalized with jaundice and ascites. She exhibited hepatosplenomegaly, severe liver dysfunction, and slight polycythemia with an increase in serum levels of beta-thromboglobin and platelet factor 4. Bone marrow was hypercellular with an increase in progenitor cells. The aggregation response of platelets to ADP and to collagen was markedly increased. Ve...
متن کاملBudd-Chiari syndrome and myeloproliferative disorder.
Budd-Chiari syndrome (BCS) is a rare clinicopathological condition characterized by occlusion of the major hepatic veins with or without membranous obstruction (MOVC)of the inferior vena cava (IVC) at its hepatic portion. Ascites, hepatomegaly and upper abdominal pain constitute the classical triad of symptoms, and the disease usually progresses to congenital liver cirrhosis and portal hyperten...
متن کاملMyeloproliferative neoplasms in Budd-Chiari syndrome and portal vein thrombosis: a meta-analysis.
Myeloproliferative neoplasms (MPNs) are the most common cause of Budd-Chiari syndrome (BCS) and nonmalignant, noncirrhotic portal vein thrombosis (PVT). In this meta-analysis, we determined the prevalence of MPNs and their subtypes as well as JAK2V617F and its diagnostic role in these uncommon disorders. MEDLINE and EMBASE databases were searched. Prevalence of MPNs, JAK2V617F, and MPN subtypes...
متن کاملinferior vena cava thrombosis in a patient with essential thrombocythemia
essential thrombocythemia is a chronic myeloproliferative disorder characterized by a sustained proliferation of megakaryocytes, which leads to increased numbers of circulating platelets. hemorrhagic and/or thrombotic episodes are frequent, and thrombosis of both veins and arteries may develop. vessels in unusual sites may be involved, e.g., the hepatic veins, mesenteric veins, and the digital ...
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ژورنال
عنوان ژورنال: Archives of hematology case reports and reviews
سال: 2021
ISSN: ['2640-7914']
DOI: https://doi.org/10.17352/ahcrr.000030