Pachydermoperiostosis (primary hypertrophic osteoarthropathy): report of a case with evidence of endothelial and connective tissue involvement.
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چکیده
منابع مشابه
Pachydermoperiostosis (primary hypertrophic osteoarthropathy): report of a case with evidence of endothelial and connective tissue involvement.
A case of pachydermoperiostosis characterised by the presence of finger clubbing, periostosis, sweating of hands and feet is described. Modifications of capillaroscopic pattern and of arteriovenous anastomoses are reported. The periungual border and finger tip tissue showed diffuse endothelial hyperplasia, hyalinosis, and sclerosis with packing of collagen fibres. Electron microscopy showed hyp...
متن کاملPachydermoperiostosis (Primary Hypertrophic Osteoarthropathy): Case Report
syndrome consisting of clubbing of the digits of the hands and feet, enlargement of the extremities secondary to periarticular and osseous proliferation, and painful and swollen joints. The condition has been divided into two categories, primary hypertrophic osteoarthropathy, also known as “pachydermoperiostosis”, and secondary hypertrophic osteoarthropathy, frequently referred to as “hypertrop...
متن کامل[Pachydermoperiostosis (idiopathic hypertrophic osteoarthropathy)].
Introduction Pachydermoperiostosis is a syndrome characterized by finger clubbing, periosteal new bone formation especially over the distal ends of long bones, and coarsening of the facial features, with thickening, furrowing and oiliness of the skin of the face and forehead. The first reported cases were the Hagner brothers, who had typical features of this syndrome. They were first described ...
متن کاملHypertrophy of the feet and ankles presenting in primary hypertrophic osteoarthropathy or pachydermoperiostosis: a case report
INTRODUCTION Pachydermoperiostosis or primary hypertrophic osteoathropathy is a rare genetic disease with autosomal transmission. This disorder, which affects both bones and skin, is characterized by the association of dermatologic changes (pachydermia or thickening of the skin) and rheumatologic manifestations (periostosis and finger clubbing). Here, we report a new observation of pachydermope...
متن کاملBilateral ptosis as a presenting feature of primary hypertrophic osteoarthropathy (pachydermoperiostosis): a case report.
Pachydermoperiostosis is a rare hereditary disorder, which affects both bones and skin. It is characterized by a combination of dermatologic changes (pachydermia or thickening of the skin) and rheumatologic manifestations (periostosis and finger clubbing). Eyelid ptosis which is caused by thickened eyelids (blepharoptosis) is a less common symptom. We report the case of a patient with a complet...
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ژورنال
عنوان ژورنال: Annals of the Rheumatic Diseases
سال: 1989
ISSN: 0003-4967
DOI: 10.1136/ard.48.3.240